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Bir Kadın Hastada Parry Romberg Sendromu: Olgu Sunumu

A FEMALE PATIENT WITH PARRY-ROMBERG SYNDROME: A CASE REPORT+

Journal Name:

  • İnönü Üniversitesi Tıp Fakültesi Dergisi

Publication Year:

  • 1999

Key Words:

Keywords (Original Language):

Author NameUniversity of AuthorFaculty of Author
Abstract (2. Language): 
A 40-year-oldd woman with left progressive hemifacial atrophy (Parry-Romberg syndrome/PRS) is reported. PRS is an unusual condition of unknown etiology, characterized by spontaneous and slowly progressive atrophy of the subcutaneous tissue and fat. We present the findings of a patient with PRS who was observed in our clinic for over four years. Ophthalmic and neurologic involvements are reviewed. The patient presented with progression of enophthalmos associated with pseudoptosis that occured secondary to intraorbital fatty atrophy, alopecia, poiosis, iris heterochromia, chronic dacryocystitis and lack of blink reflex.
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Abstract (Original Language): 
PRS'u etyolojisi belii olmayan, yüzün bir yarısında deriattı yağ ve diğer dokuların kendiliğinden yavaş seyirii llerleyici atrofisi lle karakterize nadir görülen bir tablodur. K/iniğimizde sol progressif hemifasial atrofi nedeniyle 4 ylldır takip ettiğimiz, 40 yaşında kadın hastada oftalmik ve nörolojik bulgular gözden geçirlmiştir. Hastada, intraorbital yağ dokusu atrofisine ikincil olarak geiişen ve psödoptozisin eşiik ettiği ilerleyici enoftalmus, allopesi, poiiozis, irisde heterokromi ve kırpma refleksinde kayıp saptanmıştır.
FULL TEXT (PDF): 
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  • 4
345-347
  • Turkish

REFERENCES

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