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SÎSTEMÎK LUPUS ERÎTEMATOZUS OLARAK TEDAVİ BAŞLANAN BÎR TROMBOTÎK TROMBOSÎTEMÎK PURPURA (TTP) HASTASI

A PATIENT WITH THROMBOTIC THROMBOCYTOPENIC PURPURA TREATED AS A SYSTEMIC LUPUS ERYTHEMATOSUS INITIALLY

Journal Name:

  • Türk Nefroloji, Diyaliz ve Transplantasyon Dergisi

Publication Year:

  • 1999

Key Words:

Keywords (Original Language):

Author NameUniversity of AuthorFaculty of Author
Abstract (2. Language): 
Thrombotic thrombocytopenic purpura (TTP) is a rare, life threatened disease. It is characterized by fever, variable neurological manifestations, progressive renal failure, microangiopathic hemolytic anemia and thrombocytopenia. TTP may be associated with some autoimmune diseases such as systemic lupus erythematosus (SLE). TTP may be confused with SLE because its classical sympoms such as fever, neurological manifestations, renal failure, thrombocytopenia can be seen in SLE. We report here a patient with TTP, confused with SLE, and whom the diagnosis of TTP was supported by autopsi.
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Abstract (Original Language): 
Trombotik trombositopenik purpura (TTP) nadir görülen hayatı tehdit eden bir hastalıktır. Ateş, dalgalanmalar gösteren nörolojik bozukluklar, progresif renal yetmezlik, mikroanjiopatik hemolitik anemi, trombositopeni ile karekterizedir (1). TTP, Sistemik Lupus Eritematozus (SLE) gibi otoimmun hastalıklarla birlikte olabilir. TTP 'nin klasik semptomları olan ateş, nörolojik bozukluklar, renal, bozukluklar ve trombositopeninin SLE 'de de görülmesi nedeniyle, SLE ile karışabilir. Bu olgu sunumunda ilk etapta SLE tanısı almış fakat TTP'nin klasikpentadının görülmesi ile TTP tanısı konulmuş, hasta multipl organ disfonksiyon sendromu (MODS) nedeni ile kaybedilmiş, tanısı otopsi ile desteklenmiş bir hasta tartışılacaktır.
FULL TEXT (PDF): 
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  • 1
43-45
  • Turkish

REFERENCES

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